PKAN Disease Rating Scale (PKAN-DRS)


PKAN Disease Rating Scale (PKAN-DRS)

Acronym: PKAN-DRS

Authors: Alejandra Darling, Cristina Tello, Marıa Josep Martı, Cristina Garrido, Sergio Aguilera-Albesa, Miguel Tomas Vila, Itziar Gaston, Marcos Madruga, Luis Gonzalez Gutierrez, Julio Ramos Lizana, Montserrat Pujol, Tania Gavilan Iglesias, Kylee Tustin, Jean Pierre Lin, Giovanna Zorzi, Nardo Nardocci, Loreto Martorell, Gustavo Lorenzo Sanz, Fuencisla Gutierrez, Pedro J. Garcıa, Lidia Vela, Carlos Hernandez Lahoz, Juan Darıo Ortigoza Escobar, Laura MartíSanchez, Fradique Moreira, Miguel Coelho, Leonor Correia Guedes, Ana Castro Caldas, Joaquim Ferreira, Paula Pires, Cristina Costa, Paulo Rego, Marina Magalhaes, María Stamelou, Daniel Cuadras Palleja, Carmen Rodríguez-Blázquez, Pablo Martínez-Martín, Vincenzo Lupo, Leonidas Stefanis, Roser Pons, Carmen Espinos, Teresa Temudo, and Belén Perez Dueñas

The PKAN Disease Rating Scale (PKAN-DRS) was developed to assess domains of cognition, behavior, and disability with scores based on neurological assessment of dystonia, parkinsonism, and other neurological signs in patients with pantothenate kinase-associated neurodegeneration (PKAN).

Original Publication View the Scale (PDF)

To request permission to use this Rating Scale, please fill out a Permission Request Form.

Year Published: 2017

Scale Last Updated: Unchanged since publication

Assessment Type: ClinRO

Estimated Time to Complete: 10-15 minutes

Available Translations: None

Additional Scale Publications:

Marshall RD, Collins A, Escolar ML, Jinnah H, Klopstock T, Kruer MC, Videnovic A, Robichaux‐Viehoever A, Swett L, Revicki DA, Bender RH and Lenderking WR. A scale to assess activities of daily living in Pantothenate Kinase‐Associated Neurodegeneration. Movement Disorders Clinical Practice 2019 Feb; 6(2) 139-149.

MDS-Owned Rating Scales   

Global Assessment Scale for Wilson's Disease (GAS for WD)

Global Dystonia Scale (GDS)

MDS-Unified Parkinson's Disease Rating Scale (MDS-UPDRS)

MDS Non-Motor Rating Scale (MDS-NMS)

Modified Bradykinesia Rating Scale (MBRS)

Non-Motor Symptoms Scale (NMSS)

Non-Motor Symptoms Questionnaire (NMSQ)

Non-Motor Fluctuation Assessment (NoMoFA) Questionnaire

PKAN Disease Rating Scale (PKAN-DRS)

Progressive Supranuclear Palsy Clinical Deficits Scale (PSP-CDS)

Quality of Life Essential Tremor Questionnaire (QUEST)

Rating Scale for Psychogenic Movement Disorders (PMD)

Rush Dyskinesia Rating Scale (RDRS)

Rush Video-Based Tic Rating Scale

SCales for Outcomes in PArkinson’s disease - Autonomic Dysfunction (SCOPA-AUT)

SCales for Outcomes in PArkinson’s disease – Diary Card (SCOPA-DC)

SCales for Outcomes in PArkinson’s disease – Psychiatric Complications (SCOPA-PC)

SCales for Outcomes in PArkinson’s disease – Psychosocial Functioning​ (SCOPA-PS)

SCales for Outcomes in PArkinson’s disease – Sleep (SCOPA-SLEEP)

SCales for Outcomes in PArkinson's disease-COGnition (SCOPA-COG)

Short Parkinson's Evaluation Scale (SPES)/SCales for Outcomes in PArkinson’s disease – Motor Functions (SPES/SCOPA-Motor)

UFMG Sydenham's Chorea Rating Scale (USCRS)​

Unified Dyskinesia Rating Scale (UDysRS)

Unified Dystonia Rating Scale (UDRS)

Unified Multiple System Atrophy Rating Scale (UMSARS) 

For more information about all MDS Rating Scales, please contact the International Secretariat.


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